Sugie et al. (2005) classified XMEA as a form of autophagic vacuolar myopathy, characterized by intracytoplasmic autophagic vacuoles with sarcolemmal features.The clinical course was mild; the patients suffered from slowly progressive muscle weakness mainly in the legs, but did not lose their ability to walk. There was no evidence of cardiac or neural involvement. Serum creatine kinase was elevated. By electron microscopy, an excessive number of autophagic vacuoles with staining properties of lysosomes were observed. The granular and membranous material contained in these vacuoles was actively exocytosed. The authors suggested that this disorder differed from the muscular dystrophy of Duchenne and Becker and of Emery-Dreifuss as well as from X-linked myotubular myopathy.
Rat Very low-density lipoprotein receptor (VLDLR) ELISA Kit employs a two-site sandwich ELISA to quantitate VLDLR in samples. An antibody specific for VLDLR has been pre-coated onto a microplate. Standards and samples are pipetted into the wells and anyVLDLR present is bound by the immobilized antibody. After removing any unbound substances, a biotin-conjugated antibody specific for VLDLR is added to the wells. After washing, Streptavidin conjugated Horseradish Peroxidase (HRP) is added to the wells. Following a wash to remove any unbound avidin-enzyme reagent, a substrate solution is added to the wells and color develops in proportion to the amount of VLDLR bound in the initial step. The color development is stopped and the intensity of the color is measured.
Rat Very low-density lipoprotein receptor (VLDLR) ELISA Kit listed herein is for research use only and is not intended for use in human or clinical diagnosis. Suggested applications of our products are not recommendations to use our products in violation of any patent or as a license. We cannot be responsible for patent infringements or other violations that may occur with the use of this product.
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